Cardiac involvement of Churg Strauss syndrome demonstrated by magnetic resonance imaging.

نویسندگان

  • J P Smedema
  • P van Paassen
  • M J P G van Kroonenburgh
  • G Snoep
  • H J G M Crijns
  • J W Cohen Tervaert
چکیده

Churg Strauss syndrome (CSS) may lead to cardiac involvement in up to 60% of patients. The myocardium, coronary vasculature, valves and pericardium may be affected. This results in significant morbidity and mortality, accounting for 48% of deaths due to CSS. Cardiac magnetic resonance imaging (CMR) is used to evaluate cardiac structure and function, and is able to evaluate myocardial perfusion and delineate scar tissue. We are the first to demonstrate these features in a 53-year-old CSS patient who presented with palpitations and atypical chest pains, and was found to have myocardial perfusion defects and scar tissue, most likely secondary to vasculitis of the small myocardial vasculature and myocardial infiltration.

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عنوان ژورنال:
  • Clinical and experimental rheumatology

دوره 22 6 Suppl 36  شماره 

صفحات  -

تاریخ انتشار 2004